A-Z page index

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Classical	Type I (gravis)	43% of all cases Show all EDS features including mitral valve prolapse
	Type II (mitis)	34% of all cases Mild but similar to type I
Hypermobility	Type III	10% of all cases Skin unaffected Extensive hypermobility of joints
Vascular	Type IV	6% of all cases Skin is noticeably translucent with visible veins but is not elastic Joints are unaffected Complications common and sudden death may occur at any time from large vessel rupture
Kyphoscoliosis or ocular	Type VI	2% of all cases Eye involvement Scoliosis common (curved spine)
Arthrochalasia	Type VII A and B	3% of all cases Noticeable joint hypermobility but less skin involvement Spontaneous joint dislocation common
Dermatosparaxis	Type VII C
Other	Type V	5% Extensive skin hyperelasticity with splitting, bruising and scarring
	Type VIII (periodontal)	Hyperelastic fragile skin Severe periodontitis (gum disease)
	Type IX	Skeletal defects, characteristic bony horn-like overgrowths on back part of the skull
	Type X (fibronectin deficiency)	Both rare These 2 types are so similar that they possibly should be classified together
	Type XI (benign hypermobile joint syndrome)